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Abstract. ESTOPINAN REBOLLAR, Ramón; ESTOPINAN CANOVAS, Ramón and PILA PELAEZ, Rafael. Enfermedad de Hirschsprung en un adulto. Rev Col. Resumen. LOMBANA, Luis Jorge y DOMINGUEZ, Luis Carlos. Surgery in adult Hirschsprung’s disease. Rev Col Gastroenterol [online]. , vol, n La enfermedad de Hirschsprung es una enfermedad del intestino grueso (colon). Normalmente, las heces fecales son empujadas a través del colon por.

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In this latter case, HD may affect the entire colon and even the small intestine. The analytical study was enfermevad. Case Reports Late diagnosis enfermsdad Hirschsprung’s disease. Its pages are open to the members of the Association, as well as to all members of the medical community interested in using this forum to publish their articles in accordance with the journal editorial policies.

This disorder is uncommon in adolescence and in adulthood and when present in this age group, it shows up as an ultrashort-segment disease. Department of General and Gastrointestinal Surgery. A year-old woman with an unremarkable past medical history adlutos referred to us for an anorectal manometry study due to clinical symptoms characterized by chronic constipation since infancy that did not respond to treatments with laxatives or enemas.

Case Report A year-old male was admitted in the Emergency Department by generalized abdominal pain accompanied by anorexia of several days duration.


Enfermedad de Hirschprung del adulto

Two case reports and review of the literature. Enfermedad de Hirschsprung en el adulto. Print Send to a friend Export reference Mendeley Statistics.

The pathologist’s report showed the existence of ulceration foci with acute inflammation in the submucosa. This factor contributed to the delay in her diagnosis, driving the pediatrician out of a HD hypothesis.

The patient was discharged in good general health and tolerating normal food. Zonal adult Hirschsprung’s disease. Physical examination showed a globular, asymmetrical abdomen with a 30x 15cm palpable tumor in the right abdomen.

Chromogranin detection of neuroendocrine cells: Discussion Some authors have maintained that Enfermedav disease in adults probably correspond to congenital cases not diagnosed previously, and consequently it is likely that, in fact, adult Hirschsprung’s disease does not really exist as an independent entity.

Vólvulo en adultos

SNIP measures contextual citation impact by wighting citations based on the total number of citations in a subject field. Niger J Clin Pract. For our patient, fecal incontinence is a more limiting symptom than the constipation itself, because the girl was living in constant fear of occurrence of such fact in environments like her school, which would cause great embarrassment before other people. SRJ is a prestige metric based on the idea that not all citations hirschspfung the same.

Another option in these cases is the realization of an end ileostomy following colectomy, to avoid the risk of a possible wound dehiscence, as it happened in our case.


In this case, the aganglionic segment is not removed, but a rear dissection is performed. Hirschsprung’s disease affects about 1 in 5, live births and usually presents in neonatal period. Pathogenesis of Hirschsprung’s disease. Rev Argent Resid Cir. Imaging studies such as computed tomography CT and barium enemas are usually accepted for evaluation of chronic constipation, which is a common disorder in adults.

Clinical features, diagnostics and treatment of Hirschsprung’s disease in adults. Conventional anorectal manometry trace showing the absence of the inhibitory rectoanal reflex with the maximum tolerable rectal capacity. It was later related to the absence of ganglion cells. The key finding in barium enema is the existence of a transition zone “funnel” between distal aganglionic bowel normal or narrow and proximal dilated.

Enfermedad de Hirschsprung en un adulto

Surgery was recommended, but his family did not give their permission. The treatment of choice is surgical and aganglionic segment resection and anastomosis of the healthy colonic segment to the anal canal can be performed laparoscopically.

HD occurs in approximately 1 in live births. Other proposed mechanisms include defects in the neuroblast differentiation and accelerated destruction of ganglion cells in the intestine 4.